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constituent
Unit
Total (n = 37)
correlation coefficient
Reference range
Mean ± SD
Patients exhibiting below the lower limits of the reference range (%)
Patients exhibiting values of 1.3-times or greater than the upper limits of the reference range (%)
r value
p value
Free Carnitine
μmol/L
36-74
33 ± 13
41
0
0.02
0.91
Acyl-Carnitine
μmol/L
6-23
8 ± 4
38
0
−0.24
0.15
1-Methyl-histidine
nmol/mL
<9.1
5 ± 5
0
8
−0.09
0.66
3-Methyl-histidine
nmol/ml
TRA-8.2
4 ± 2
0
5
−0.30
0.08
Alanine
nmol/mL
258.8-615.2
458 ± 130
3
8
0.24
0.15
Anserine
nmol/ml
ND
ND
0
0
-
-
Arginine
nmol/mL
31.8-149.5
128 ± 32
0
27
−0.27
0.10
Asparagine
nmol/ml
43.8-90.6
56 ± 11
19
0
−0.23
0.17
Aspartic acid
nmol/mL
TRA-7.2
5 ± 2
0
5
0.08
0.63
Carnosine
nmol/mL
ND
ND
0
0
-
-
Citrulline
nmol/mL
17.9-48.0
45 ± 12
0
27
−0.42
0.01*
Cystathionine
nmol/mL
ND
2 ± 0
0
73
−0.09
0.66
Cystin
nmol/mL
4.7-34.8
19 ± 11
3
14
−0.25
0.14
Ethanolamine
nmol/mL
TRA-10.5
7 ± 2
0
3
0.15
0.37
Glutamate
nmol/mL
12.2-82.7
122 ± 59
0
68
0.44
〈0.01*
Glutamine
nmol/mL
418.0-739.8
700 ± 128
0
38
−0.41
0.01
Glycine
nmol/mL
140.4-427.3
394 ± 102
0
38
−0.54
〈0.01*
Hdroxylysine
nmol/mL
ND
ND
0
ND
-
-
Histidine
nmol/mL
63.0-105.2
94 ± 15
0
27
0.00
0.99
Homocystine
nmol/mL
ND
ND
0
0
-
-
Hydroxyproline
nmol/mL
TRA-18.8
17 ± 5
0
27
−0.30
0.10
Isoleucine
nmol/mL
37.0-100.4
78 ± 15
0
8
−0.07
0.67
Leucine
nmol/mL
74.2-169.1
134 ± 25
0
8
0.05
0.76
Lysine
nmol/mL
125.7-281.9
237 ± 44
0
22
−0.30
0.08
Methionine
nmol/mL
15.5-38.6
30 ± 5
0
8
−0.14
0.40
Ornithine
nmol/mL
42.6-141.2
86 ± 25
0
3
−0.05
0.78
Phenylalanine
nmol/mL
43.5-79.8
59 ± 9
0
3
0.02
0.91
Phosphoethanol-amine
nmol/mL
TRA
TRA
0
0
-
-
Proline
nmol/mL
71.3-373.0
289 ± 241
0
11
−0.16
0.36
Sarcosine
nmol/mL
TRA
8 ± 3
0
51
−0.34
0.15
Serine
nmol/mL
91.5-186.4
168 ± 34
0
24
−0.04
0.81
Taurine
nmol/mL
46.4-128.2
110 ± 43
3
35
−0.15
0.37
Threonine
nmol/mL
74.2-216.1
144 ± 35
0
3
−0.15
0.39
Tryptophan
nmol/mL
36.2-79.3
37 ± 10
59
0
0.35
0.03*
Tyrosine
nmol/mL
38.4-89.4
72 ± 18
0
16
0.18
0.28
Valine
nmol/mL
156.2-360.4
248 ± 41
0
0
−0.02
0.89
α-aminoadipic acid
nmol/mL
ND
ND
0
0
-
-
α-amino-n-butyric acid
nmol/mL
8.1-31.0
35 ± 8
0
70
−0.10
0.06
β-Alanine
nmol/mL
TRA-11.8
2 ± 1
0
0
0.05
0.88
β-Amino-iso-butyric acid
nmol/mL
<5.9
3 ± 2
0
5
−0.18
0.32
γ-Amino-nbutyric acid
nmol/mL
ND
ND
0
0
-
-
The correlation between the concentration of ammonia and each item is presented. A p -value of 0.05 was regarded as significant
TRA Trace
ND Not detectable
*: p < 0.05